One case of myxoid glioneuronal tumor in the left frontal lobe

Abstract Myxoid glioneuronal tumor (MGNT), previously described as dysembryoplastic neuroepithelial tumor (DNET) of the septum pellucidum, was classified as a new tumor type in the fifth edition of the WHO Central Nervous System Tumor Classification of 2021. This classification was based on its anatomical location, imaging features, and genetic characteristics. Myxoid glioneuronal tumors are clinically rare and prone to misdiagnosis. In this report, we present a case of myxoid glioneuronal tumor in the left frontal lobe, which was confirmed through surgical pathology.