Low-grade endometrial stromal sarcoma: case report

Introduction: Endometrial stromal sarcoma is a rare tumor that corresponds to approximately 1% of uterine tumors. Its diagnosis is challenging to make due to the similarity with benign tumors both in the characteristics of the lesion in imaging exams and about the symptoms, which is only obtained from the histopathological analysis. Case report: In the case reported, to obtain the diagnosis was necessary several attempts and methods, and the patient was in an advanced stage, with distant metastasis, impairing her prognosis. This article discusses ways to diagnose, staging, prognosis, and management of this rare neoplasm.