Rapidly Progressive Primary Scleroderma Cardiomyopathy in a Young Adult Characterized by Multimodality Imaging.

Samuel D Maidman, Joav Birjiniuk,Robert Donnino,Atreyee Basu, H Michael Belmont, Randal I Goldberg,Bernard S Kadosh

CASE (Philadelphia, Pa.)(2023)

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摘要
•Scleroderma-related heart disease is usually secondary to lung disease or PH.•Scleroderma rarely causes systolic HF in young patients or those without CAD.•A multimodality strategy should be used to characterize scleroderma cardiomyopathy.
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关键词
cardiomyopathy,multimodality imaging
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