Congenitally corrected transposition of the great arteries

Congenitally corrected transposition of the great arteries has an estimated prevalence of 0.5% of clinically diagnosed congenital malformations of the heart. Congenitally corrected transposition is characterized by chambers that are joined discordantly at the atrioventricular junction and ventricles that are joined discordantly at the ventriculo-great arterial junction–atrioventricular alignments and ventriculoarterial alignments are both discordant. The double discordance–atrioventricular and ventriculoarterial–physiologically corrects the discordance intrinsic to each. However, this does result in a systemic right ventricle, a tricuspid valve in the systemic position, and long-term issues with atrioventricular conduction.