Reevaluating the Evolution of Vertebrobasilar Dolichoectasia (VBD) Through Pacak-Zhuang Syndrome

Journal of neurological surgery(2023)

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摘要
Introduction: Vertebrobasilar dolichoectasia (VBD) is a lengthening (dolicho) and widening (ectasia) of vertebrobasilar arteries. The basilar artery is often tortuous in VBD. Collagen vascular disorders, tumors, and glycogen storage disorders are associated with VBD. Genetic mechanistic studies of VBD are lacking. Furthermore, the diagnostic criteria, phenotypes, pathophysiology, and evolution vary according to VBD etiology.
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关键词
vertebrobasilar dolichoectasia,syndrome,pacak-zhuang
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