Thoracic follicular dendritic cell sarcoma- an outlandish presentation of a rare tumour with review of literature

Follicular dendritic cell sarcoma is a rare low grade malignant neoplasm that arises from follicular dendritic cells in lymphoid tissue germinal centres and accounts for 0.4% of all soft tissue sarcomas. It is extremely rare to have pulmonary follicular den-dritic cell sarcoma with endobronchial extension and as an anteri-or mediastinal mass with mediastinal lymph node involvement. We present the case of a 34-year-old male non-smoker who had been experiencing chest pain for three months. A lobulated left peri-hilar mass with endobronchial spread into the left main bronchus and mediastinal lymphadenopathy was identified on chest CT. The bronchoscope-guided cryobiopsy of the endo-bronchial mass was inconclusive. After a thorough multidiscipli-nary discussion, the patient underwent left sided pneumonectomy, mediastinal mass resection, and systematic lymph node dissec-tion. Histologic examination using immunohistochemistry revealed follicular dendritic cell sarcoma.