Long-term evaluation of pulmonary function and survival of patients with interstitial pneumonia with autoimmune features.

Julio A Huapaya,Afroditi Boulougoura,Julie Fried, Sepehr Mesdaghinia, Brooks J Culotta,Sara Carson, Peter J Bergquist,Pranay Krishnan, Haijun Wang,Cristina Reichner,Virginia Steen

Clinical and experimental rheumatology(2023)

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摘要
Long-term pulmonary function and six-minute walk test remained stable over 36 months in our IPAF cohort. Prognosis and pulmonary function in UIP had similar outcomes compared to non-UIP. Although 40% of IPAF patients could not be sub-classified, our exploratory subclassification stratified 60% of patients into a CTD-like subgroup.
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关键词
interstitial pneumonia with autoimmune features,connective tissue diseases,pulmonary function,usual interstitial pneumonia
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