Liver Transplantation For Hepatic Epithelioid Hemangioendothelioma: A Case Report And Literature Review

Background: Hepatic epithelioid hemangioendothelioma (HEHE) is a rare tumor with incidence less than one per million. Due to low incidence of the disease, the risk factors, mechanism of the disease, treatment therapy and prognosis are not studied enough. Case presentation: Herein, we report a case of female patient who was diagnosed as HEHE and received liver transplantation in our center. She underwent the first deceased liver transplantation on 26th December 2013 in our center. Fifteen months later, she presented with yellow skin and sclera. She was diagnosed as intrahepatic biliary stricture. Both drug therapy and endoscopic nasobiliary drainage failed. She underwent retransplantation at last on 22nd August 2015. She recovered well and kept in good condition until now. Conclusion: Hepatic epithelioid hemangioendothelioma (HEHE) is an indication of liver transplantation. Long term survival after liver transplantation can be achieved.