Case Report Of A Rare Presentation Of Perirenal Primitive Neuroectodermal Tumor

Primitive neuroectodermal tumors (PNETs) belong to a group of highly malignant central nervous system tumors that are composed of small, round, undifferentiated neuroectodermal cells. The current study reports a case of perirenal PNET in a 25-year-old female. The tumor presented as an adrenal tumor and caused symptoms of left waist and back pain, which increased over a 2-month period. Open surgery was performed to achieve radical mass resection. The pathological and immunohistochemical diagnosis confirmed that the tumor was a perirenal PNET, which had spread into nervous and adrenal tissue. To our knowledge, the present case of perirenal PNET is the first to be reported in PubMed.