Metastatic dysgerminoma in a young patient with 46 XY DSD: A rare case report

•A rare case of metastatic dysgerminoma in a young patient with 46XY DSD.•Incidence of DSD is 1:5000 with 90% of patients having 46XX chromosome and only 10% have 46 XY chromosome.•Individuals with an underlying DSD, especially with Y chromosome have an increased risk of developing germ cell tumor.•Dysgerminoma is highly chemosensitive tumor.•Multidisciplinary approach is required in management of such cases.