Structural Abnormalities on Cardiac Magnetic Resonance Imaging in Patients With Catecholaminergic Polymorphic Ventricular Tachycardia.

JACC: Clinical Electrophysiology(2020)

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摘要
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an inherited ion channel disorder characterized by exertional or stress-induced polymorphic ventricular arrhythmias and sudden death. Post-mortem genetic testing implicates CPVT in a significant portion of autopsy-negative sudden deaths
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