Moya Moya In Children: About 2 Cases

Introduction Moya Moya is a rare chronic intracranial arterial disease that affects internal carotid arteries. It is characterized by a progressive occlusion of the end portions of the internal carotids with the development of a locum circulation. Cases report Two cases of Moya Moya have been reported. They were a 9 years old male and a 6 ½ years old female. Both children had a history of ischemic stroke revealed in one case by right hemiparesis, and in the other case by transient bilateral blindness. The first child had a stroke in the left superficial sylvian artery at the age of 2.5 years, with no thrombogenic pathology or haemostasis disorder. He received an anti platelet aggregation and practiced motor rehabilitation. He consulted after 6 years for generalized tonic-clonic seizures with behavioral disorder and mental confusion. The angio MRI showed multiple systemic vascular accidents dealing with the diagnosis of Moya Moya. The second child had at the initial brain scan a recent occipital ischemic hypodensity with multiple porencephalic cavities probably sequellar in bi frontal and anterior arm of the right internal capsule. Then she reconsulted after 3 months for a recurrence of blindness associated with an alteration of the state of consciousness. A brain MRI showed the presence of multiple strokes of different ages. The diagnosis of Moya Moya was confirmed by cerebral palsy. Both children had severe sequelae. Conclusion Moya Moya is a rare but serious chronic cerebrovascular disease in young children. The diagnostic delay is frequent, related to its polymorphous symptomatology. The diagnosis is based on Angio CT and Angio MRI brain which are requested in 1st intention. It must be evoked in front of repetitive vascular accidents of children of different ages.