Diagnostic Utility of Complement Serology for Atypical Hemolytic Uremic Syndrome.

Mayo Clinic Proceedings(2018)

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摘要
A COMS abnormality should not be interpreted in isolation. In conjunction with clinical presentation, a decrease in both CFB and CH50 may be an important clue to support the diagnosis of aHUS.
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关键词
aHUS,AP,C3,C5,C3G,CFB,CFH,CFI,COMS,ELISA,G6P,HRP,HUS,MAC,ROC,SCR,SLE,sMAC,TMA,TPE,TTP,VUS
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