Non-Compaction Cardiomyopathy. Risk Stratification of Sudden Death for Automatic Cardioverter Defibrillator Implantation

SUMMARY Non-compaction cardiomyopathy is a rare disease. Its natural history includes heart failure, thromboembolic events, arrhythmias and sudden death (SD). In the absence of data from randomized studies or records, the ACC / AHA / HRS 2008 guidelines recommend the automatic implantable cardioverter defibrillator (AICD) in all patients with non-compaction cardiomyopathy to reduce the risk of suden death. Objective Describe the outcomes of patients with non-compaction cardiomyopathy according to selected criteria for risk stratification of sudden death to decide the implantation of an AICD. Material and Methods A total of 80 patients were analyzed. The diagnosis was established by echocardiography and nuclear cardiac magnetic resonance imaging criteria. The criteria for implantation of an AICD as a secondary prevention included sudden death and sustained ventricular tachycardia (SVT); as primary prevention included left ventricular ejection fraction (LVEF) < 30% or ≥ 2 risk factors (family history of sudden death [FHSD], syncope and non-sustained VT). Background