Resection of a large cystic cervical lymphatic malformation complicated by severe postoperative necrotizing enterocolitis

Here, we report on a patient with severe postoperative intestinal complications after the resection of a prenatally diagnosed large cervical lymphatic malformation. To elucidate the pathogenesis of this life-threatening complication, we analyzed this case as part of a matched pair. The mature index patient was delivered by Caesarean section, and the postnatal adaption was unimpaired. Surgical resection was performed on the 11th day of life. Intralesional bleeding was identified as the most important risk factor in the development of protracted shock and postoperative necrotizing enterocolitis.