Should Prostacycline Be the First Line Treatment of PAA in Patients With PAH

PURPOSE: Pulmonary artery aneurysm (PAA) is a rare disease. Proximal PAA occasionally induces some serious complications, including compression of the bronchus, dissection and/or rupture of the pulmonary artery, as well as a thrombus of the pulmonary artery. Recently, with the development of new drugs, the prognosis of patients with PAH has improved. We present a case of a patient with proximal PAA with severe PAH and successfully treated with treprostinil