Klippel-Trenaunay Syndrome and Left Iliac Vein Agenesis

This case report describes a patient with Klippel-Trenaunay syndrome (KTS) and a rare deep venous anomaly, agenesis of the left iliac veins. A dilated suprapubic vein was confirmed by duplex ultrasound assessment and by phlebography to be draining his left lower limb into his right iliac veins. The management options and implications are discussed.